Most men with EDMD survive into middle age, although a defect in the heart's rhythm (heart block) may be fatal if not treated with a pacemaker.
A pacemaker is a device that sends small electrical impulses to the heart muscle to maintain a suitable heart rate.
Elton is an epileptic, and in 1999, he was diagnosed with an irregular heartbeat and fitted with a pacemaker.
Irregularities in heartbeat may be treated with medication or a pacemaker.
A pacemaker may be implanted if these do not provide adequate control.
A permanent pacemaker or implantable cardioverter defibrillator (ICD) is sometimes needed to regulate the child's heart rhythm.